Phaeochromocytoma and paraganglioma
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Authors
Tarling , J.A
Kumar, R
Ward, L.J
Boot , C
Wassif, WS
Issue Date
2024
Type
Scientific Paper
Language
Keywords
Research Subject Categories::VETERINARY MEDICINE::Pathology
Alternative Title
Abstract
Abstract
Phaeochromocytomas and paragangliomas are rare catecholamine-producing neuroendocrine tumours which can potentially cause catastrophic crises with high morbidity and mortality. This best practice article considers the causes and presentation of such tumours, screening and diagnostic tests, management of these patients and consideration of family members at risk.
Keywords: Adrenal Glands; CATECHOLAMINES; Endocrine System Diseases; Neuroendocrine Tumors.
© Author(s) (or their employer(s)) 2024. No commercial re-use. See rights and permissions. Published by BMJ.
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Conflict of interest statement
Competing interests: None declared.
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Publication types
Review
MeSH terms
Adrenal Gland Neoplasms* / diagnosis
Adrenal Gland Neoplasms* / pathology
Adrenal Gland Neoplasms* / therapy
Catecholamines / metabolism
Humans
Paraganglioma* / diagnosis
Paraganglioma* / pathology
Pheochromocytoma* / diagnosis
Pheochromocytoma* / pathology
Substances
Catecholamines
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Citation
Tarling JA, Kumar R, Ward LJ, Boot C, Wassif WS. Phaeochromocytoma and paraganglioma. J Clin Pathol. 2024 Jul 18;77(8):507-516. doi: 10.1136/jcp-2023-209234. PMID: 38453430.